CJD

Question 1

what

Answer 1

rapidly progressing neurological condition caused by prion proteins

Question 2

what do proin protiens do

Answer 2

induce formation of amyloid folds resulting in tightly packed beta-pleated sheets resistant to proteases

Question 3

features

Answer 3

rapid onset dementia

myoclonus

Question 4

Ix

Answer 4

EEG
MRI
tonsil biopsy

Question 5

EEG findings

Answer 5

biphasic high amplitude sharp waves

Question 6

MRI findings

Answer 6

hyperintense signals in basal ganglia and thalmus