Dermatofibrosarcoma protuberans

Question 1

Tissue sarcoma arising in the dermis and often penetrates into fat.
■ Etiology is unknown but has been reported to arise in scars. It is caused by a translocation between
chromosome 17 and 22.

Answer 1

Dermatofibrosarcoma protuberans

Question 2

Peak age

Answer 2

20-50 yo

Question 3

Presentation

Answer 3

non specific plaque often resembling a keloid w purplish to brown ish coloration

Question 4

histo

Answer 4

a spindle cell proliferation often arranged as whorls

so-called herring bone pattern

Question 5

Tx

Answer 5

mohs micrographic sx.
RT
In resection; prognosis is good