Periportal halo / periportal collar sign
Zone of low attenuation around the intrahepatic portal veins on contrast enhanced CT
Hypoechogenicity on liver US same distribution
Likely represents periportal oedema
Type 1 Caroli
Simple Caroli disease
Congenital disorder of multifocal cystic dilation of segmental intrahepatic bile ducts. Classified as type V choledochal cyst.
Cystic dilation of larger intrahepatic bile ducts
Type II Caroli
Caroli syndrome
Congenital disorder of multifocal cystic dilation of segmental intrahepatic bile ducts. Classified as type V choledochal cyst.
Combination of small bile duct dilatation and congenital hepatic fibrosis or cirrhosis +/- portal hypertension
Caroli disease association
Medullary sponge kidney
ARPKD
(Very rarely) ADPKD