What is the most common cause of pulmonic stenosis?
Congenital
What is the most rare and unlikely cause of pulmonic stenosis?
Rheumatic fever
Is carcinoid heart disease, a cause for pulmonic stenosis
Yes
What is carcinoid heart disease?
A tumor that is secreting high levels of serotonin.
This can cause congestive heart failure, affect the valves and cause right sided failure
What other things can cause pulmonic stenosis?
-Pulmonic stenosis of Peripheral junction of the right and left pulmonary arteries
-Infundibular(Subvalvular)
-Prosthetic valve dysfunction
Infundibular just means?
Subvalvular
What is Noonan syndrome?
A cardio facial genetic syndrome that causes heart problems, short facial features, and other issues
What disease is classified as a genetic cardio facial syndrome?
Noonan syndrome
Noonan syndrome is classified with what three cardiac things?
Pulmonic stenosis
HCM
ASD (30%)
What percentage of patients with Noonan -syndrome have an ASD
30 %
With pulmonic stenosis, what secondary issues occur
Systolic pressure overload leads to RVH
Regional hypertrophy may lead to?
Infundibular stenosis
With Pulmonic stenosis the ___ chamber usually remains normal and it’s the ____ chamber that will enlarge
RV ; RA
What is a big physical symptom of pulmonic stenosis?
Dyspnea on exertion
What is the murmur for pulmonic stenosis?
Systolic ejection murmur -left upper sternal border
With pulmonic stenosis m-mode may show an increase in what?
Increase in the a dip
What is pulmonic stenosis What occurs on m mode with the a dip?
A dip increases
If the a- dip on m mode of a pulmonic valve increases more than 7 mm. What do we consider this?
Severe PS
Describe the pulmonic valve differences on m mode between pulmonic stenosis and pulmonary hypertension
PS = increased a dip (>7mm is severe PS)
PHTN= flying “w” a dip decreases
In which direction do the pulmonic valve tether with pulmonic stenosis?
Systolic doming or tethering for PS
Pulmonic stenosis can cause post stenotic ____ of the pulmonary artery
Dilation
With infundibular pulmonic stenosis, what is narrowed
RVOT
Pulmonic stenosis does ___ cause PHTN
NOT
Pulmonic stenosis causes ___ and right side ___ it does not cause ____
CHF; dilation ;PHTN