Photodermatology

Question 1

what is porphyria?

Answer 1

these are a group of disorders within the body where there is a problem in the production of haem

Question 2

name some of the main porphyrias?

Answer 2

phototoxic
blistering and skin porphyrias
acute attack
severe congentital

Question 3

typical presentations

Answer 3

blisters
fragility
hyperpigmentation
hypertrichosis
solar urticaria
morphoea

Question 4

what can cause PCT (porphyria cutanea tarda)

Answer 4

alcohol
haemochromatosis
viral hepatits
oestrogens