Thalassaemia
Gallstones
Expanded bones
Haemosiderosis with low signal on MRCP in liver, pancreas, bones
Polysplenism, left isomerism
Typically diagnosed later than asplenia as less severe cardiac disease, more commonly acyanotic than asplenia Female predominant Bilateral hyparterial bronchi Bilateral bilobed lungs Multiple splenules Dextrocardia 37% PAPVR, TAPVR in 70% Midgut malrotation 80% Gallbladder agenesis 50% Renal and pancreatic abnormalities Azygous IVC very common
10% biliary atresia
Asplenia
Association with cardiac disease e.g. tricuspid atresia
TAPVR almost 100%
Other renal and GI and vascular associations
Renal TB
.