Ivacaftor (CFTR gene therapy)
Aims to improve ion flow and increase the activity of remaining CFTR gene
Bronchial wall thickening & airway dilatation (bigger than the vessel adjacent)
Bronchiectasis
Lymphatic interstitial pneumonitis (LIP) is associated with which conditions?
RA
Sicca syndrome
Bronchiectasis
Tree in bud distal airways disease
Non-tuberculous mycobacterium diseases
Asthma + central bronchiectasis
ABPA
Bronchodilator response
12%
200ml