Carbomyl Phosphate + Ornithine ->
Citrilline + PPi
In Mitochondria
Citrilline leaves Mito Membrane
2ATP + NH4 + HCO3 ->
Carbomyl Phosphate
Enzyme: Carbomyl Phosphate Synthase
Regulated by N-Acetyl Glutamate
Citrulline + Aspartate + ATP ->
Argino-Succinate + PPi + AMP
2 ATPs are basically expended
In Cytosol
Argino-Succinate ->
Fumarate + Arginine
Arginine + H2O ->
Urea + Ornithine
Ornithine renters mitochondria