risser scale
uses standing AP radiographs to determine the progress of ossification of the Anterior Superior iliac spine
transverse deficiency
limb developed typically to a particular level
skeletal elements do not exist past a certain level
distal buds may be present
longitudinal deficiency
reduction or absence of an element occurs withtin the long axis of a alimb
skeletal elements may be present distal to the affected bones
named by describing bones in a proximal to distal sequence and states whether each affected bone is totally or partially absent
proximal femoral focal deficiency
PFFD
absence or hypoplasia of the proximal femur
may include acetabulum, femoral head, patella, tibia, fibula
U/L or B/L
proximal femoral focal deficiency
clinical manifestations
shortened thigh held in flexion, ABD, ER
Hip and knee contractures
Severe LLD
causes of congential limb deficiencies
genetic
vascular (disruption of arterial flow)
teratogenic (thalidomide, contraceptives)
amniotic bands
Which limb is often invloved with CLD?
upper limb
most transverse deficiences are U/L or B/L?
U/L
rudimentary finger vestiges called ‘nubbins” can be present
aquired amputations
trauma
trauma from machinery, power tools, MVA, gun shot, railroad
peak in summer/early fall
acquired limb deficiencies
pathologies
ewing’s sarcoma and osteosarcoma
Ewing sarcoma family of tumors
neuroepithelial tumors that involve both the bone and soft tissue
occur in flat and long bone, common in pelvis, ribs, femur, humerus, tibia
seen in peak growth rates
osteosarcoma
primary malignant tumor of bone
occurs with growth spurt
located in metaphyseal portion of rapidly growing bone
* distal femur
* proximal tib
* proximal humerus
Dx of osteosarcoma/ewing’s sarcoma
pain @ site of tumor
systemic symptoms common with ESFT
chronic pain with negative history of injury/trauma and w/o musculoskeltal abnormality
radiolgic eval
MRI
biopsy/histologic exam
CT scan
what is an alternative to amputation in malignant tumors?
limb sparing or limb salvage procedures
limb sparing or limb salvage procedures
involve resection of tumor and reconstruction of limb to preserve function
* use of excision of bone and replacement with allograft and endoprosthetic implant
amputation
level of skeletal immaturity and future growth
physes preserved
terminal overgrowth of periosteum
limb revisions purpose
done to perform fit or function of a prosthesis
types of limb revisions
knee arthrodesis and amputation
limb lengthenening techniques and/or ephysiodesis of the involved or uninvolved limb
rotationplasty
rotationplasty
for congenital limb deficiencies or w/ bony tumors
excision of distal femur/proximal femur
180° rotation of residual lower limb
preserves most of RL and NV supply
benefits of rotationplasty
increased LL
imrpove prosthetic function (ankle serves as knee joint)
decrease in problems with bony overgrowth
decrease in pain from PL
allows for growth